{"id":7181,"date":"2017-08-23T12:14:07","date_gmt":"2017-08-23T12:14:07","guid":{"rendered":"https:\/\/jurmed.ro\/medici\/?p=7181"},"modified":"2017-08-25T10:06:52","modified_gmt":"2017-08-25T10:06:52","slug":"cardiomiopatia-hipertrofica-obstructiva","status":"publish","type":"post","link":"https:\/\/jurmed.ro\/medici\/cardiomiopatia-hipertrofica-obstructiva\/","title":{"rendered":"Cardiomiopatia hipertrofic\u0103 obstructiv\u0103"},"content":{"rendered":"<p style=\"text-align: justify\"><strong>Cardiomiopatia hipertrofic\u0103 obstructiv\u0103.\u00a0<\/strong><strong>Ce nout\u0103\u0163i sunt pentru bolnavii \u015fi cardiologii rom\u00e2ni?<\/strong><\/p>\n<p style=\"text-align: justify\"><em>Interviu cu Gheorghe CERIN, medic primar cardiolog, doctor \u00een \u015ftiin\u0163e medicale, \u015feful\u00a0 Departamentului de Cardiologie \u015fi Medicin\u0103 Intern\u0103, Clinica San Gaudenzio Novara, Italia, si cardiolog consultant la Cardiac Center, Spitalul Monza, Bucure\u015fti<\/em><\/p>\n<p style=\"text-align: justify\"><strong>D-le Dr Cerin, mi se pare c\u0103 \u00een ultima vreme v-a\u0163i schimbat preferin\u0163ele profesionale: de la o pasiune mai veche pentru valvulopatii vedem c\u0103 v-a\u0163i orientat aten\u0163ia spre cardiomiopatia hipertrofic\u0103. Pentru c\u0103 \u00een luna mai 2015 era\u0163i la Sibiu, fiind unul din referen\u0163ii la Simpozionul Interna\u0163ional privind Cardiomioptia Hipertrofic\u0103, iar \u00een decembrie 2015 era\u0163i prezent \u00een Spania cu o sesiune live \u00een box dedicat\u0103 tot acelea\u015fi boli, la Sevilia &#8211; Euro Echo 2015,pentru ca \u00een aprilie 2016 s\u0103 prezidia\u0163i \u00eempreun\u0103 cu prof Ioan Bruckner o sesiune special\u0103 pe aceea\u015fi tem\u0103 la Congresul Na\u0163ional de Medicin\u0103 Intern\u0103, C\u0103lim\u0103ne\u015fti \u2013 2016, iar \u00een acest an, la CNC Sinaia s\u0103 participa\u0163i de asemenea la sesiunea dedicat\u0103 cardiomiopatiei hipertrofice, \u00eempreun\u0103 cu prof Bogdan Popescu. Cum se explic\u0103 orientarea Dvs c\u0103tre aceast\u0103 boal\u0103 aparent rar\u0103, pentru c\u0103 de fapt \u015ftim c\u0103 este mai frecvent\u0103 dec\u00e2t se consider\u0103? Cum se face c\u0103 sunte\u0163i mai tot timpul \u00een prezen\u0163a d-lui prof Paolo Ferrazzi \u015fi a prof Paolo Spirito? Ce v\u0103 leag\u0103 de d\u00e2n\u015fii \u015fi \u00een ce \u00eemprejur\u0103ri v-a\u0163i cunoscut?<\/strong><\/p>\n<p style=\"text-align: justify\">R\u0103spunsul este simplu &#8211; apropierea \u015fi interesul pentru aceast\u0103 patologie a venit progresiv,tocmai pentru c\u0103 \u00een ultimul timp am avut ocazia s\u0103 cunosc mai bine echipa prof Ferrazzi \u015fi prof Spirito \u015fi mai ales pe cei doi incontestabili mae\u015ftri. Deoarece lucr\u0103m \u00eempreun\u0103 \u00een Italia \u0163n acela\u015fi Grup de Spitale \u00abPoliclinico di Monza\u00bb, era fiziologic dac\u0103 vre\u0163i ca o dat\u0103 ce ne-am \u00eent\u00e2lnit s\u0103 \u015fi colabor\u0103m. Pentru c\u0103 avem profile profesionale convergente \u015fi interese comune legate de chirurgia pe cord deschis \u2013 eu ca ecocardiografist \u00een chirurgie cardiac\u0103 \u015fi cardiolog clinic, iar prof Ferrazzi ca \u015fi chirurg cardiac, cu o via\u0163\u0103 \u00eentreag\u0103 dedicat\u0103 acestei meserii. Cum se \u015ftie cardiomiopatia hipertrofic\u0103 merit\u0103 toat\u0103 aten\u0163ia noastr\u0103, a tuturor, pentru c\u0103 este boala cardiac\u0103 genetic\u0103 cea mai frecvent\u0103 (1:500 \u00een popula\u0163ia general\u0103 adult\u0103), fiind caracterizat\u0103 \u00een general prin hipertrofia asimetric\u0103 de sept interventricular \u015fi adeseori de obstruc\u0163ie intraventricular\u0103. Este \u00een plus boala care ucide prin moarte subit\u0103 cei mai mul\u0163i sportivi \u015fi oameni tineri, oameni aparent s\u0103n\u0103to\u015fi care aveau boal\u0103,ins\u0103 nu \u015ftiau din p\u0103cate, pentru c\u0103 nu fuseser\u0103 diagnostica\u0163i \u00een timp util.<\/p>\n<p style=\"text-align: justify\">Referitor la prof Ferrazzi, pentru colegii care nu se ocup\u0103 de cardiomiopatia hipertrofic\u0103, a-\u015fi vrea s\u0103 amintesc de la \u00eenceput c\u0103 este singurul chirurg cardiac care a operat un num\u0103r de peste 450 de bolnavi cu CMHO ca prim operator! \u00cen ultimii ani la Centrul de Cardiomiopatii de la Policlinico di Monza din Italia, sunt opera\u0163i anual \u00eentre 80 \u015fi 100 de bolnavi cu CMHO. Aceasta a f\u0103cut ca Grupul italian de la Monza s\u0103 se situeze \u00een pole position \u00een Europa, c\u00e2\u015ftig\u00e2nd \u00een timp o incontestabil\u0103 experien\u0163\u0103 clinic\u0103 \u00een CMHO. Iar experien\u0163a aceasta este greu de g\u0103sit \u00een general \u00een lume; \u00eencep\u00e2nd cu diagnosticul genetic, cu evaluarea riscului de moarte subit\u0103 \u2013 unde putem conta pe experien\u0163a prof Paolo Spirito, cu diagnosticul imagistic perioperator, dar mai ales privind lansarea unor tehnici chirurgicale \u00een CMHO.<\/p>\n<p style=\"text-align: justify\">Cred c\u0103 ar mai trebui subliniat \u00een plus faptul c\u0103 majoritatea centrelor din lume opereaz\u0103 doar c\u00e2teva cazuri de CMHO anual &#8211; sau chiar deloc \u00een unii ani, cum este \u015fi cazul nostru, la Clinica San Gaudenzio din Novara. La cei 5\/600 de bolnavi opera\u0163i anual pe cord deschis la San Gaudenzio,doar c\u00e2\u0163iva bolnavi sunt cu CMHO. Este demonstrat \u00eens\u0103 c\u0103 mortalitatea \u015fi complica\u0163iile post operatorii \u00een chirurgia CMHO sunt influenta\u0163e direct de num\u0103rul de cazuri operate \u00een centrul respectiv. American Journal of Cardiology a publicat \u00een anul 2014 un articol pe aceast\u0103 tem\u0103 cu 665 de bolnavi opera\u0163i \u00eentre 1998 \u015fi 2010 \u00een spitale americane care aveau \u00een 82% un volum operator mare, din care 77% erau centre universitare sau echivalente. Studiul arat\u0103 o mortalitate medie de 5,9% \u015fi o rat\u0103 a complica\u0163iilor de 30%, \u00een aceste centre care, repet, nu erau dedicate bolnavilor cuCMHO \u015fi care operau ace\u015fti bolnavi ocazional, cum se \u00eent\u00e2mpl\u0103 \u015fi la noi \u00een Rom\u00e2nia \u015fi mai peste tot \u00een lume.<\/p>\n<p style=\"text-align: justify\">Mortalitatea operatorie \u00een centrele care fac chirurgie dedicat\u0103 pe CMHO este \u00eens\u0103 de aproape cinci &#8211; \u015fase ori mai mic\u0103, \u015fi nu dep\u0103\u015fe\u015fte cifra de 1%. De aceea experien\u0163a acumulat\u0103 \u00eentr-un asemenea centru poate influen\u0163a direct propor\u0163ional rezultatul chirurgical iar colaborarea bilateral\u0103 cu un centru dedicat CMHO nu poate fi dec\u00e2t benefic\u0103 pentru to\u0163i: medici \u015fi bolnavi.<\/p>\n<p style=\"text-align: justify\"><strong>Dle dr, v\u0103d c\u0103 Dvs vorbi\u0163i cu mult\u0103 seninatate \u015fi convingere despre tratamentul chirurgical, de\u015fi \u00een ultimele dou\u0103 decenii vedem c\u0103 se practic\u0103 din ce \u00een ce mai mult tratamentul interven\u0163ional, prin alcoolizarea percutanat\u0103 a arterelor coronare responsabile de zon\u0103 de hipertrofie. De ce Dvs ave\u0163i aceast\u0103 preferin\u0163\u0103 pentru sala de opera\u0163ie \u015fi nu pentru tratamentul interven\u0163ional, sau crede\u0163i c\u0103 eu gre\u015fesc \u015fi c\u0103 este doar o impresie a mea?<\/strong><\/p>\n<p style=\"text-align: justify\">A\u015f zice c\u0103 nu gresi\u0163i! Vede\u0163i dvs cam \u00eentotdeauna sala de opera\u0163ie ne sperie\u2026 Pe to\u0163i! Mai pu\u0163in poate pe chirurgi c\u0103 sunt mai obi\u015fnui\u0163i cu ea, dar sperie pe cardiologi, pe medici \u015fi pe bolnavi \u00een general\u2026 Este dac\u0103 vre\u0163i \u00een firea omului s\u0103 reac\u0163ioneze a\u015fa\u2026 De\u015fi producerea unui infarct acut de miocard la bolnavii cu CMHO prin injectarea de alcool \u00een coronare ucide la fel de mult ca interven\u0163ia chirurgical\u0103 \u2013 \u015fi chiar mai mult dup\u0103 cum demonstreaz\u0103 multe studii, bolnavii \u015fi chiar medicii prefer\u0103 \u00een ultima vreme tratamentul interven\u0163ional. \u00cen aceste \u00eent\u00e2lniri de care vorbea\u0163i Dvs, noi am avut ca invitat pe d-l dr Seggeweiss Hubert din Germania, al\u0103turi de Prof Paolo Ferrazzi \u015fi Paolo Spirito. Cum se \u015ftie, \u00een ultimele dou\u0103 decenii \u015fcoala german\u0103 este cea care a promovat metoda de alcoolizarea septala \u015fi dr Seggeweiss \u00een mod special.<\/p>\n<figure id=\"attachment_7183\" aria-describedby=\"caption-attachment-7183\" style=\"width: 300px\" class=\"wp-caption alignleft\"><a href=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-1.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-7183 size-medium\" src=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-1-300x169.jpg\" alt=\"\" width=\"300\" height=\"169\" srcset=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-1-300x169.jpg 300w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-1.jpg 627w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-7183\" class=\"wp-caption-text\"><em>Echipa italorom\u00e2n\u0103 \u00een Sala Operatorie la Monza, Italia &#8211; Dr. L. Dorobantu (st\u00e2nga), dr. Cristina C\u0103ld\u0103raru, Prof. P. Ferrazzi, dr. G. Cerin, dr. Ruxandra Jurcut, dr. D. Poggio<\/em><\/figcaption><\/figure>\n<figure id=\"attachment_7185\" aria-describedby=\"caption-attachment-7185\" style=\"width: 300px\" class=\"wp-caption alignright\"><a href=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-2.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-7185 size-medium\" src=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-2-300x212.jpg\" alt=\"\" width=\"300\" height=\"212\" srcset=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-2-300x212.jpg 300w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-2.jpg 693w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-7185\" class=\"wp-caption-text\"><em>Prof. Ferrazzi, dr. Cristina C\u0103ld\u0103raru, dr. L. Doroban\u021bu, Prof. P. Spirito \u0219i Dr. Cerin &#8211; discu\u021bia preoperatorie a cazului la Spitalul Monza, Bucure\u0219ti<\/em><\/figcaption><\/figure>\n<p style=\"text-align: justify\">R\u0103spunsul \u2018tehnic\u2019 \u00eens\u0103 la \u00eentrebarea dvs nu \u00eel dau eu, ci ghidurile americane \u015fi europene care consider\u0103 tratamentul chirurgical ca prim\u0103 alegere \u015fi pun alcoolizarea septal\u0103 pe planul doi la bolnavii cu CMHO. Trebuie reamintit \u00eens\u0103 c\u0103 numai bolnavii intens simptomatici, care au obstruc\u0163ie intraventricular\u0103 cu gradient mare &#8211; de peste 50mmHg, au indica\u0163ie de tratament interven\u0163ional sau chirurgical. Bolnavii care devin asimptomatici cu tratament medical (sau care sunt \u00een clasa NYHA 1-2) \u015fi au gradient mai mic de 50mmHg (provocat sau \u00een repaus) trebuie trata\u0163i medical \u015fi urm\u0103ri\u0163i clinic. \u00cen opinia dr Seggeweiss ca \u015fi a prof Ferrazzi \u015fi Spirito, cu tot\u0163ii prezen\u0163i la discu\u0163ii \u00een aceste \u00eent\u00e2lniri, cele dou\u0103 metode de tratament trebuie considerate de fapt complementare. Deoarece \u00een chirurgia cardiac\u0103 v\u00e2rsta bolnavului este direct corelat\u0103 cu decesul, exist\u0103 tendin\u0163a spre tratamentul interven\u0163ional la persoanele v\u00e2rstnice, mai ales c\u00e2nd au patologie asociat\u0103, dac\u0103 au desigur criterii de selec\u0163ie compatibile cu alcoolizarea septal\u0103. Tratamentul chirurgical este de aceea mai frecvent indicat la bolnavii tineri, pe baza rezultatelor bune demonstrate \u00een cei peste 50 de ani de experien\u0163\u0103 mondial\u0103 \u015fi de follow up cu bolnavii opera\u0163i prin tehnica de miectomie Morrow. Fa\u0163\u0103 de alcoolizare, \u00een plus chirurgia pe cord deschis permite \u015fi rezolvarea insuficien\u0163ei mitrale\u2013 de regul\u0103 prin repararea valvei, regurgitare care este frecvent asociat\u0103 la bolnavii cu CMHO \u015fi care r\u0103m\u00e2ne nerezolvat\u0103 c\u00e2nd se opteaz\u0103 pentru alcoolizarea septal\u0103. Pentru a alege ca metod\u0103 de tratament alcoolizarea este nevoie \u00een plus de o selec\u0163ie foarte atent\u0103 \u015fi special\u0103 a bolanvilor iar ecocardiografia cu mediu de contrast ultrasonic intracoronarian a adus \u00een ultimii ani o contribu\u0163ie esen\u0163ial\u0103 \u00een selec\u0163ia bolnavilor candidabili sau nu latratamentul interven\u0163ional.<\/p>\n<p style=\"text-align: justify\"><strong>A\u015fadar metoda se practic\u0103! Care este experien\u0163a Dvs \u00een Italia cu alcoolizarea septal\u0103? Care sunt rezultatele?<\/strong><\/p>\n<figure id=\"attachment_7186\" aria-describedby=\"caption-attachment-7186\" style=\"width: 300px\" class=\"wp-caption alignleft\"><a href=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-3.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-7186 size-medium\" src=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-3-300x249.jpg\" alt=\"\" width=\"300\" height=\"249\" srcset=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-3-300x249.jpg 300w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-3.jpg 546w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-7186\" class=\"wp-caption-text\"><em>Prof. Ferrazzi, dr. Cerin \u0219i Prof Spirito la Euro Echo 2015, Sevilia<\/em><\/figcaption><\/figure>\n<p style=\"text-align: justify\">La Clinica San Gaudenzio din Novara alcoolizarea septal\u0103 nu este folosit\u0103. \u015ei asta de foarte mul\u0163i ani de zile; cu siguran\u0163\u0103 de peste 15 ani. La Novara, bolnavii cu CMHO care \u00een ciuda tratamentului medical maximal r\u0103m\u00e2n\u00a0 simptomatici, \u015fi au obstruc\u0163ie intraventricular\u0103 spontan\u0103 sau provocat\u0103, cu gradient peste 50mmHg, merg \u00een sala de opera\u0163ie pentru miectomie (Morrow operation). Cum aminteam \u015fi mai \u00eenainte, ca peste tot \u00een lume, oper\u0103m c\u0103teva cazuri de CMHO pe an. \u00cempreun\u0103 cu Dr Diena Marco am operat \u00een ace\u015fti ani la Novara \u015fi c\u00e2\u0163iva bolnavi tineri din Rom\u00e2nia, care erau foarte simptomatici, \u00een clasa 3 \u015fi 4 NYHA, dar care ast\u0103zi, la 5-6 ani de F-up sunt bine, stabili \u015fi \u00een clasa NYHA 1-2. Eu am v\u0103zut \u00een Italia primele cazuri de CMHO tratate cu embolizare septal\u0103 cu alcool \u00een urm\u0103 cu peste dou\u0103 zeci de ani (1994 \u2013 1997, \u201998), la Spitalul San Donato din Milano, pe atunci cel mai mare centru de cardiochirurgie italian. Prof Luigi Inglese \u015fi dr Tao Onorato au renun\u0163at progresiv la metoda alcooliz\u0103rii septale dup\u0103 ce au f\u0103cut o prim\u0103 duzin\u0103 de bolnavi, deoarece rezultatele nu erau cele a\u015fteptate \u015fi nu se puteau compara cu rezultatele pe care le ob\u0163ineam prin interven\u0163ia chirurgical\u0103 pe cord deschis. Ast\u0103zi, \u00een general \u00een Italia metoda alcooliz\u0103rii \u00een CMHO este rar \u015fi sporadic utilizat\u0103.<\/p>\n<p style=\"text-align: justify\"><strong>\u00cen\u0163eleg din ce spune\u0163i c\u0103 problema \u015fi gestionarea acestei boli este deosebit de complex\u0103\u2026 Care este situa\u0163ia la noi? Cum suntem organiza\u0163i \u00een Rom\u00e2nia? Cine se ocup\u0103 de ace\u015fti bolnavi? Care sunt centrele cu experien\u0163\u0103 pe acest profil?<\/strong><\/p>\n<p style=\"text-align: justify\">De\u015fi eu nu mai sunt tot timpul prezent \u00een Rom\u00e2nia de mul\u0163i ani de zile, \u015fi de aceea a\u015f putea avea o percep\u0163ie fragmentar\u0103 asupra acestui argument, a\u015f zice c\u0103 \u00een Rom\u00e2nia, ca \u015fi \u00een restul Europei, aproape \u00een fiecare centru de chirurgie cardiac\u0103 se opereaz\u0103 doar sporadic cazuri de CMHO \u015fi tot ocazional unele centre mai fac c\u00e2teodat\u0103 alcoolizare septal\u0103. Nu avem un centru dedicat pentru CMHO \u00eens\u0103; sau mai bine zis nu am avut un asemenea centru p\u00e2n\u0103 \u00een urm\u0103 cu un an circa. Ar mai fi desubliniat \u00eens\u0103 c\u0103 Europa are destul de pu\u0163ine centre dedicate tratamentului chirurgical al CMHO: Monza (peste 85 cazuri pe an), Roterdam (peste 25 cazuri\/an), Londra, Lisabona, Sevilia, Florenta, Milano \u2013 San Raffaele (\u00eentre 15 \u015fi 25 cazuri\/an). La nivel interna\u0163ional se consider\u0103 prin conven\u0163ie c\u0103 un spital poate fi catalogat ca fiind centru dedicat tratamentului chirurgical al CMHO atunci c\u00e2nd acesta opereaz\u0103 un num\u0103r de 25 de cazuri de cardiomiopatie obstructiv\u0103 pe an.<\/p>\n<p style=\"text-align: justify\">Lucr\u00e2nd cu Prof Ferrazzi \u015fi cu Prof Spirito \u00een cadrul aceluia\u015fi Grup de Spitale, \u00eempreun\u0103 cu d\u00e2nsul \u015fi echipa acestuia, dup\u0103 ce am operat la \u00eenceput sporadic bolnavi cu CMHO \u00een Rom\u00e2nia,\u00een 2015 am g\u00e2ndit c\u0103 a sosit momentul s\u0103 realiz\u0103m la Spitalul Monza din Bucure\u015fti, un prim Centru Dedicat Cardiomiopatiei Hipertrofice.\u00a0 \u00cen ultimul an \u015fi jum\u0103tate s-a format astfel la Spitalul Monza primul nucleu de medici dedica\u0163i bolnavilor cu CMHO, mai ales celor candida\u0163i interven\u0163iei chirurgicale: chirurg cardiac dedicat plus anestezist, cardiolog ecocardiografist dedicat al\u0103turi de un radiolog dedicat examenului de rezonan\u0163\u0103 magnetic\u0103 cardiac\u0103, pentru c\u0103 examenul RMN este crucial \u00een stabilirea planningului chirurgical. Dr Lucian Doroban\u0163u este chirurgul care a operat \u00een aceast\u0103 perioad\u0103 \u00eempreun\u0103 cu Prof Ferrazzi primii 20 de bolnavi cu rezultate comparabile cu cele de la nivel interna\u0163ional. Echipa CMHO, format\u0103 din dr Lucian Doroban\u0163u -coordonatorul echipei, dr Ana Fruntelat\u0103, dr C\u0103ld\u0103r\u0103u Cristina, dr Alexandrescu Maria s-a format \u00eens\u0103 prin training intensiv at\u00e2t \u00een Italia (la Monza) c\u00e2t \u015fi la Bucure\u015fti. La \u00eenceput prof Ferrazzi a venit\u00a0 \u00een Rom\u00e2nia \u00eenso\u015fit de colegii s\u0103i italieni (dr Poggio, dr Khouri, etc), dar ast\u0103zi echipa rom\u00e2n\u0103 este complet independent\u0103 \u2013 de la evaluarea complex\u0103 pre \u015fi post operatorie, p\u00e2n\u0103 la efectuarea interven\u0163iei. Ne lipse\u015fte \u00eenc\u0103 echipa \u015fi laboratorul de analize genetice, care necesit\u0103 o logistic\u0103 mult mai complex\u0103, dar pe care o avem \u00een calcul pentru viitor. Din p\u0103cate \u00een Rom\u00e2nia nu avem pentru moment nici un centru care face analize genetice la bolnavii cu cardiomiopatii.<\/p>\n<p style=\"text-align: justify\">Trebuie \u00eens\u0103 subliniat c\u0103 meritul primului Registru Na\u0163ional al bolnavilor cu Cardiomiopatie Hipertrofic\u0103 apar\u0163ine d-lui prof Apetrei Eduard de la Fundeni, registru care exist\u0103 \u015fi azi \u015fi pe care d\u00e2nsul \u00eel coordoneaz\u0103 \u015fi \u00een prezent. Colaboratorii d\u00e2nsului, Prof Bogdan Popescu, dr Ro\u015fca Monica \u015fi mai apoi dr Jurcut Ruxandra au continuat aceast\u0103 initia\u0163iv\u0103 iar ast\u0103zi avem o prim\u0103 eviden\u0163\u0103 on line a unora dintre ace\u015fti bolnavi. Nu sunt mul\u0163i \u00eens\u0103; maxim 200 de cazuri \u00eenregistrate, ceea ce este extrem de pu\u0163in dac\u0103 lu\u0103m \u00een calcul datele de statistic\u0103 1:500, adic\u0103 circa 35-40.000 de cazuri cu CMH \u00een Rom\u00e2nia, din care circa 15.000 ar fi bolnavi cu form\u0103 obstructiv\u0103 \u00een repaus. Cum se \u015ftie, obstruc\u0163ia intraventricular\u0103 este prezent\u0103 \u00een repaus la circa 1\/3 din bolnavii cu cardiomiopatie hipertrofic\u0103. Prin teste de provocare \u00eens\u0103 (efort fizic sau manvera Valsalva), o alt\u0103 treime din ace\u015fti bolnavi pot demonstra fenomene de obstruc\u0163ie intracardiac\u0103, ceea ce implic\u0103 tratamentul chirurgical sau interven\u0163ional, dac\u0103 nu r\u0103spund suficient de bine la tratament medical (beta blocante \u00een principal, uneori verapamil).<\/p>\n<p style=\"text-align: justify\">Este cazul s\u0103 amintim pe aceast\u0103 cale colegilor care au \u00een \u00eengrijire bolnavi cu CMH \/ CMHO c\u0103 sunt invita\u0163i c\u0103lduros s\u0103 \u00eenregistreze aceste cazuri pe site-ul dedicat: <a href=\"http:\/\/www.rencmh.ro\/\">http:\/\/www.rencmh.ro<\/a>. Sigur c\u0103 aceasta implic\u0103 un consum de timp pentru \u00eenregistrarea cazurilor on line, dar numai astfel noi medicii vom putea avea o viziune clar\u0103 privind soarta acestor bolnavi \u00een Rom\u00e2nia \u015fi vom putea vedea care sunt rezultatele cu tratamentul medical, interven\u0163ional sau chirurgical.<\/p>\n<p style=\"text-align: justify\"><strong>Spunea\u0163i mai \u00eenainte c\u0103 prof Ferrazzi are contribu\u0163ii personale privind abordarea chirurgical\u0103 a bolnavilor cu CMHO. Pute\u0163i fi mai concret? Despre ce este vorba? Ce nout\u0103\u0163i \u015fi avantaje aduc noile tehnici chirurgicale?<\/strong><\/p>\n<figure id=\"attachment_7187\" aria-describedby=\"caption-attachment-7187\" style=\"width: 300px\" class=\"wp-caption alignleft\"><a href=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-4.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-7187 size-medium\" src=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-4-300x200.jpg\" alt=\"\" width=\"300\" height=\"200\" srcset=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-4-300x200.jpg 300w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/Cardiomiopatia-hipertrofic\u0103-4.jpg 450w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-7187\" class=\"wp-caption-text\"><em>Prof. P. Ferrazzi la Congresul Na\u021bional de Medicin\u0103 Intern\u0103, Calim\u0103ne\u0219ti 2016<\/em><\/figcaption><\/figure>\n<p style=\"text-align: justify\">D-l profesor Ferrazzi are dou\u0103 contribu\u0163ii personale \u00een tratamentul chirurgical al CMHO: prima este o tehnic\u0103 personal\u0103 de reparare a mitralei prin rezecarea corzilor foi\u0163ei anterioare iar\u0103 dou\u0103este efectuarea miectomiei Morrow prin rezecarea unei singure piese \u2013 \u2018one piece myectomy\u2019. Este printre foarte pu\u0163inii chirurgi cardiaci care face miectomia dintr-o singur\u0103 pies\u0103. Trebuie subliniat c\u0103 miectomia Morrow este o procedur\u0103 chirurgical\u0103 deosebit de dificil\u0103, pentru c\u0103 \u00een timpul principal al opera\u0163iei chirurgul nu are nici un reper vizual direct \u00een zona efectiv\u0103 de lucru \u015fi practic nu vede lama bisturiului atunci c\u00e2nd sec\u0163ioneaz\u0103 septul intraventricular&#8230; O simte doar! Pentru c\u0103 tractul de ie\u015fire al ventriculului st\u00e2ng, unde se opereaz\u0103, este foarte str\u00e2mt. Totul se bazeaz\u0103 pe meticulozitate \u015fi pe un al \u201c\u015faselea simt\u201d al chirurgului, care trebuie s\u0103 \u00ee\u015fi construiascp un model tridimensional mental foarte precisal zonei pe care o rezecp. De aceea majoritatea chirurgilor prefer\u0103 s\u0103 efectueze miectomia dup\u0103 tehnica mai simpl\u0103 &#8211; \u201cpiece by piece\u201d. Am v\u0103zut \u00een ace\u015fti ani c\u0103 prof Ferrazzi \u00eembin\u0103 imaginile ecocardiografice (transtoracice dar mai ales transesofagiene intraoperatorii) cu cele de mare precizie ob\u0163inute la Cine RMN cardiac \u015fi, a\u015f mai ad\u0103uga, cu o via\u0163\u0103 \u015fi o experien\u0163\u0103 de chirurg dedicate acestei boli. RMN cardiac la Monza (ca \u015fi la Bucure\u015fti) a devenit metoda absolut indispensabil\u0103 \u00een construirea acestei imagini mentale virtuale din mintea chirurgului. Numai astfel \u00eei este posibil chirurgului s\u0103 efectueze miectomia dintr-o singur\u0103 bucat\u0103 (foto), f\u0103r\u0103 ca el s\u0103 vad\u0103 de fapt \u00een mod direct zona din sept pe care o sec\u0163ioneaz\u0103. Evident c\u0103 exist\u0103 un risc mare de perforare a septului, dar dup\u0103 ani de experien\u0163\u0103 \u015fi sute de bolnavi opera\u0163i vedem c\u0103 a\u015fa ceva nu se \u00eent\u00e2mpl\u0103.<\/p>\n<p style=\"text-align: justify\">Al doilea aspect este legat de contribu\u0163ia esen\u0163ial\u0103 a prof Ferrazzi la repararea valvei mitrale la bolnavii cu CMHO. \u00cen luna octombrie 2015 JACC (66; 15, 1687 \u2013 96) a publicat aceast\u0103 tehnic\u0103 absolut inovativ\u0103 privind rezec\u0163ia corzilor tendinoase secundare de pe foi\u0163a mitral\u0103 anterior\u0103. Prof Valentin Fuster, Editor \u00een Chief al JACC, \u00een editorialul din acela\u015fi num\u0103r, consider\u0103 aceast\u0103 opera\u0163ie ca fiind o tehnic\u0103 revolu\u0163ionar\u0103 (\u201cfascinating, striking, breakthrough technique\u201d), care va marca \u00een mod indiscutabil de aici \u00eencolo chirurgia CMHO. Este de re\u0163inut c\u0103 multe centre, unele chiar cu renume la nivel mondial, nu obi\u015fnuiesc s\u0103 fac\u0103 repararea mitrale \u015fi \u00eent\u00e2lnim uneori bolnavi tineri opera\u0163i de CMHO care r\u0103m\u00e2n cu proteze mecanice pentru toat\u0103 via\u0163a, cu dezavantajele de rigoare ale unei proteze mecanice.<\/p>\n<figure id=\"attachment_7190\" aria-describedby=\"caption-attachment-7190\" style=\"width: 300px\" class=\"wp-caption alignright\"><a href=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/cardiomiopatie.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"wp-image-7190 size-medium\" src=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/cardiomiopatie-300x174.jpg\" alt=\"\" width=\"300\" height=\"174\" srcset=\"https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/cardiomiopatie-300x174.jpg 300w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/cardiomiopatie-768x446.jpg 768w, https:\/\/jurmed.ro\/medici\/wp-content\/uploads\/sites\/2\/2017\/08\/cardiomiopatie.jpg 782w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-7190\" class=\"wp-caption-text\"><em>Prof P Ferrazzi, dr Cristina Caldararu, Prof Spirito, dr Cerin, Dr Antonela Muresan, Dr L Dorobantu, in ATI Sp Monza, la unul di cei 20 de bolnavi cu CMHO operati la Bucuresti<\/em><\/figcaption><\/figure>\n<p style=\"text-align: justify\">Inutil s\u0103 v\u0103 spun c\u0103 ambele tehnici au fost scrpulos implementate \u015fi \u00een noul Centru de Cardiomiopatii de la Spitalul Monza din Bucure\u015fti, dr Lucian Doroban\u0163u devenind progresiv independent \u015fi familiar \u00een efectuarea acestor opera\u0163ii, care, a\u015fa cum se poate vedea, sunt deosebit de complexe \u015fi cer mult\u0103 expertiz\u0103 din partea \u00eentregii echipe. Trebuie \u00eens\u0103 subliniat c\u0103 numai prin munca asidua, prin \u015fi mai mult\u0103 pasiune \u015fi o foarte str\u00e2ns\u0103 colaborare \u00eentre cele dou\u0103 echipe a fost posibil\u0103 crearea \u00eentr-un timp record a unui astfel de Centru, despre care a\u015f zice c\u0103 Rom\u00e2nia avea cu siguran\u0163\u0103 mare nevoie. Ar mai trebui poate s\u0103 spunem c\u0103 ast\u0103zi \u00een lume mai to\u0163i chirurgii din centerele dedicate, care se opereaz\u0103 CMHO sunt persoane trecute de v\u00e2rst\u0103 adult\u0103 \u00een marea lor majoritate \u015fi de aceea se simte acut nevoia unui transfer genera\u0163ional. De aceea ne place s\u0103 credem c\u0103 la spitalul Monza din Bucure\u015fti dl prof Ferrazzi prin formarea acestei echipe \u015fi a chirurgului a realizat de fapt un schimb genera\u0163ional profesional, pentru care \u00eei mul\u0163umim \u00eenc\u0103 o dat\u0103 \u00een numele colegilor de la Monza \u015fi a actualilor \u015fi viitorilor bolnavi.<\/p>\n<p style=\"text-align: justify\">\n","protected":false},"excerpt":{"rendered":"<p>Cardiomiopatia hipertrofic\u0103 obstructiv\u0103.\u00a0Ce nout\u0103\u0163i sunt pentru bolnavii \u015fi cardiologii rom\u00e2ni? Interviu cu Gheorghe CERIN, medic primar cardiolog, doctor \u00een \u015ftiin\u0163e medicale, \u015feful\u00a0 Departamentului de Cardiologie \u015fi Medicin\u0103 Intern\u0103, Clinica San [&hellip;]<\/p>\n","protected":false},"author":4,"featured_media":7192,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[276],"tags":[],"class_list":["post-7181","post","type-post","status-publish","format-standard","has-post-thumbnail","category-interviu"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.0 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Cardiomiopatia hipertrofic\u0103 obstructiv\u0103 - Jurmed - Medici<\/title>\n<meta name=\"description\" content=\"acest aicol vorbeste despre cardiomiopatia hipertrofic\u0103\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/jurmed.ro\/medici\/cardiomiopatia-hipertrofica-obstructiva\/\" \/>\n<meta property=\"og:locale\" content=\"ro_RO\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cardiomiopatia hipertrofic\u0103 obstructiv\u0103 - 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